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Prion Disease Associated With Diarrhea and Autonomic Neuropathy

(Prion Protein Systemic Amyloidosis)

By

Pierluigi Gambetti

, MD, Case Western Reserve University

Last full review/revision Jun 2020| Content last modified Jun 2020
Click here for the Professional Version

Prion disease associated with diarrhea and autonomic neuropathy is a newly discovered prion disease that initially affects nerves outside the brain, causing diarrhea and loss of feeling in the feet.

Prion disease associated with diarrhea and autonomic neuropathy differs from other prion diseases as follows:

The disease progresses over decades. People may live up to 30 years after symptoms develop.

There is no cure at present. Treatment focuses on relieving symptoms.

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