Comparing Types Of Idiopathic Interstitial Pneumonias*
Comparing Types Of Idiopathic Interstitial Pneumonias*
Disorder | People Most Often Affected | Percentage of Affected People Who Smoke Cigarettes | Treatment | Outlook |
|---|---|---|---|---|
Idiopathic pulmonary fibrosis | More frequently, men over 50 | More than 60% | Pulmonary rehabilitation Lung transplantation Pirfenidone or nintedanib | 50–70% die in 5 years. |
Desquamative interstitial pneumonia | More frequently, men aged 30–50 | More than 90% | Smoking cessation Corticosteroids | 5% die in 5 years. |
Nonspecific interstitial pneumonia | More frequently, women aged 40–60 | Fewer than 40% | Corticosteroids | Fewer than 50% die in 5 years. |
Cryptogenic organizing pneumonia | People of any age, usually aged 40–50 | Fewer than 50% | Corticosteroids | Two thirds completely recover, but the disorder recurs in many. Death is rare. |
Respiratory bronchiolitis–associated interstitial lung disease | People aged 30–50 (slightly more men) | More than 90% | Smoking cessation Corticosteroids | Death is rare. |
Acute interstitial pneumonia | People of any age | Unknown | Best treatment unknown | 60% die in less than 6 months. |
Lymphoid interstitial pneumonia | Mostly women of any age | Unknown | Corticosteroids | The prognosis is difficult to predict. |
Idiopathic pleuroparenchymal fibroelastosis | People of any age (median age 57) | Usually non-smokers | Best treatment unknown (possibly corticosteroids) | Disease progresses in 60% of people. |
* In decreasing order of frequency. | ||||