Merck Manual

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Primary Lymphedemas

Primary Lymphedemas

Disorder

Age at Symptom Onset

Comments

Congenital lymphedema

Before age 2 years

Milroy disease, a subtype, also causes jaundice (yellowing of the skin) and diarrhea.

Lymphedema praecox

2–35 years

Typically occurs in women at the onset of menses

Meige disease, a subtype, also causes the person to have extra eyelashes, cleft palate, and swelling of the legs, arms, and face.

Lymphedema tarda

After age 35

Some (but not all) affected people may have family members with this disorder.