Idiopathic pulmonary fibrosis
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More frequently, men over 50
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Pirfenidone or nintedanib
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Desquamative interstitial pneumonia
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More frequently, men aged 30–50
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Nonspecific interstitial pneumonia
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More frequently, women aged 40–60
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Fewer than 50% die in 5 years.
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Cryptogenic organizing pneumonia
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People of any age, usually aged 40–50
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Two thirds completely recover, but the disorder recurs in many.
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Respiratory bronchiolitis–associated interstitial lung disease
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People aged 30–50 (slightly more men)
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Acute interstitial pneumonia
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60% die in less than 6 months.
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Lymphoid interstitial pneumonia
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The prognosis is difficult to predict.
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Idiopathic pleuroparenchymal fibroelastosis
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People of any age (median age 57)
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Best treatment unknown (possibly corticosteroids)
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Disease progresses in 60% of people.
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