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Immunodeficiency Disorders
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Immunodeficiency Disorders
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Overview of Immunodeficiency Disorders
Primary Immunodeficiencies
Humoral immunity deficiencies
Cellular immunity deficiencies
Combined humoral and cellular immunity deficiencies
Phagocytic cell defects
Complement deficiencies
Primary immunodeficiency references
Secondary Immunodeficiencies
Geriatrics Essentials
Key Points
Approach to the Patient With Suspected Immunodeficiency
Manifestations of immunodeficiency
Evaluation
History
Physical examination
Initial testing
Additional testing
Prenatal and neonatal diagnosis
Evaluation reference
Prognosis
Treatment
Infection prevention
Management of acute infection
Replacement of missing immune components
Investigational therapy
Treatment references
Key Points
Ataxia-Telangiectasia
Symptoms and Signs
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Treatment
Key Points
Chédiak-Higashi Syndrome
Symptoms and Signs
Diagnosis
Treatment
Chronic Granulomatous Disease (CGD)
Symptoms and Signs
Symptoms and signs reference
Diagnosis
Treatment
Key Points
Chronic Mucocutaneous Candidiasis
Symptoms and Signs
Diagnosis
Treatment
Key Points
Common Variable Immunodeficiency (CVID)
Symptoms and Signs
Diagnosis
Treatment
Treatment reference
DiGeorge Syndrome
Symptoms and Signs
Diagnosis
Treatment
Treatment reference
Hyper-IgE Syndrome
Symptoms and Signs
Diagnosis
Treatment
Hyper-IgM Syndrome
X-linked hyper-IgM syndrome
Autosomal recessive hyper-IgM syndrome
Diagnosis
Treatment
Selective IgA Deficiency
Symptoms and Signs
Diagnosis
Prognosis
Treatment
Key Points
Leukocyte Adhesion Deficiency
Symptoms and Signs
Diagnosis
Treatment
Selective Antibody Deficiency With Normal Immunoglobulins (SADNI)
Diagnosis
Treatment
Severe Combined Immunodeficiency (SCID)
Symptoms and Signs
Diagnosis
Treatment
Key Points
Transient Hypogammaglobulinemia of Infancy
Wiskott-Aldrich Syndrome
Symptoms and Signs
Diagnosis
Treatment
X-linked Agammaglobulinemia
Diagnosis
Treatment
X-linked Lymphoproliferative Syndrome
Symptoms and Signs
Diagnosis
Treatment
ZAP-70 Deficiency
Diagnosis
Treatment