Merck Manual

Please confirm that you are not located inside the Russian Federation

honeypot link

Prion Disease Associated With Diarrhea and Autonomic Neuropathy

(Prion Protein Systemic Amyloidosis)

By

Pierluigi Gambetti

, MD, Case Western Reserve University

Last full review/revision Jun 2020| Content last modified Jun 2020
CLICK HERE FOR THE PROFESSONAL VERSION

Prion disease associated with diarrhea and autonomic neuropathy is a newly discovered prion disease that initially affects nerves outside the brain, causing diarrhea and loss of feeling in the feet.

Prion disease associated with diarrhea and autonomic neuropathy differs from other prion diseases as follows:

The disease progresses over decades. People may live up to 30 years after symptoms develop.

There is no cure at present. Treatment focuses on relieving symptoms.

NOTE: This is the Consumer Version. DOCTORS: CLICK HERE FOR THE PROFESSONAL VERSION
CLICK HERE FOR THE PROFESSONAL VERSION
Others also read
Test your knowledge
Intracerebral Hemorrhage
An intracerebral hemorrhage is bleeding inside the brain and is considered a medical emergency. Which of the following is often the most common initial symptom of an intracerebral hemorrhage?
Download the Manuals App iOS ANDROID
Download the Manuals App iOS ANDROID
Download the Manuals App iOS ANDROID

Also of Interest

Download the Manuals App iOS ANDROID
Download the Manuals App iOS ANDROID
Download the Manuals App iOS ANDROID
TOP